Sturge-Weber syndrome

Case contributed by Dr Ian Bickle

Presentation

Female in 30's presents to A and E following a seizure.

Patient Data

Age: 30 years
CT

Gyriform calcification in the high left frontal lobe, with the characteristic 'tram-track' calcification.

Associated parenchyma volume loss.

Disproportionately large left frontal sinus compared to the right.

Choriod plexus symmeterical.

Case Discussion

Sturge Weber syndrome is one form of phakamatosis, characterised by a pial haemangioma in the brain with an associated facial haemangioma.

The leptomeningeal haemangioma results in a vascular steal affecting the subjacent cortex and white matter producing localised ischaemia, hence the associated parenchymal volume loss.

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Case information

rID: 26281
Case created: 11th Dec 2013
Last edited: 8th Mar 2017
Inclusion in quiz mode: Included

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