Endocardial fibroelastosis

Endocardial fibroelastosis (EFE) is a rare cardiac condition which is classically described in the paediatric population (typically first two years). It is one of the causes for infants to present with unexplained heart failure. 

Pathology

The condition results from increasing amounts of fibrous and elastic tissue affecting the endocardium as well as the sub endocardium. This then causes diffuse thickening with subsequent impairment of myocardial contractility. 

Assocations

Radiographic features

Ultrasound

Echocardiography may show:

Share article

Article Information

rID: 10531
Section: Pathology
Tag: cases
Synonyms or Alternate Spellings:
  • Endocardial fibroelastosis (EFE)
  • Right-sided endocardial fibroelastosis

Support Radiopaedia and see fewer ads

Updating… Please wait.
Loadinganimation

Alert accept

Error Unable to process the form. Check for errors and try again.

Alert accept Thank you for updating your details.