Eosinophilic fasciitis

Eosinophilic fasciitis (EF), also known as Shulman syndrome, is an uncommon connective tissue disorder.

It can potentially present at age. There is a recognized female predilection 3,4.

Patients typically present with pronounced extremity oedema and skin induration. 

Clinical features include

Eodinophilic fasciitis tends to involve the limbs.

Tends to demonstrate muscular fascial plane thickening without any myositis. Changes are generally symmetrical. Signal changes include 1,3:

  • T2 FS/STIR: high signal compared to muscle involving fascial planes
  • T1 C+ (Gd): shows fascicle enhancement

Tends to respond to corticosteroids with excellent response.

First described by L E Shulman et al. in 1975 2.

Imaging differential considerations include:

  • necrotising fasciitis: tends to have accompanying fluid/gas collections/abscess formation, cellulitis and muscle inflammation
Share article

Article information

rID: 10777
Tag: cases, cases
Synonyms or Alternate Spellings:
  • Shulman syndrome
  • Shulman's syndrome

Support Radiopaedia and see fewer ads

Cases and figures

  • Drag
    Case 1
    Drag here to reorder.
  • Drag
    Case 2
    Drag here to reorder.
  • Updating… Please wait.

    Alert accept

    Error Unable to process the form. Check for errors and try again.

    Alert accept Thank you for updating your details.