Intrasphenoidal encephalocele

Intrasphenoidal encephaloceles represent encephaloceles which extend into the sphenoid sinus yet confined by its floor 1.

Patients present with spontaneous cerebral spinal fluid (CSF) rhinorrhea. 

Intrasphenoidal encephaloceles are divided into medial perisellar and lateral sphenoid recess encephaloceles 2 

  • medial perisellar encephaloceles occur within the sphenoid sinus and are more common
  • lateral sphenoid encephaloceles are rare and are usually associated with lateral pneumatization of the sphenoid sinus into the pterygoid recesses

Contributing factors to lateral intrasphenoid encephalocele include arachnoid pits/weaknesses in the skull base and intracranial hypertension 4 

  • CSF pressure and the hydrostatic pulsative forces may lead to the development of pit holes on the middle fossa at the sites of arachnoid villi with herniation of dura/arachnoid or brain tissue 5 
  • If those defects are located over pneumatized lateral extension of the sphenoid sinus, encephalocele can develop and lead to CSF leakage into the sinus 6

Congenital lateral intrasphenoidal encephaloceles occur secondary to persistence of the Sternberg's canal and are located medial to the foramen rotundum 7.

CT

CT cisternography demonstrate sphenoid sinus pneumatization, a defect in the superior wall of the left lateral recess of the sphenoid sinus and anteromedial temporal lobe herniating through the bony defect.

MRI

MR cisternography is a non-invasive technique which can reveal CSF leakage in multiple planes. On T2-weighted spin-echo sequence, the bright CSF signal is well apperciated against the signal void air of the paranasal sinuses 1.

Encephalocele

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Article information

rID: 48895
Section: Pathology
Tag: cases
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    Case 1: lateral intrasphenoidal encephalocele
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