Parachordomas are rare neuroepithelial tumors with glial differentiation that are histologically similar to chordomas but do not occur in the axial skeleton.
They are generally slow growing and non-disseminating, and sometimes have late local recurrence after resection.
They usually occur in the deep soft tissues of the extremities or in the skin. Occasionally they may occur in the retroperitoneum.
They have a nonspecific imaging appearance on CT and MRI. Calcifications may be visualized in the masses at CT.