Congenital pulmonary airways malformation

Case contributed by Dr Jeremy Jones

Presentation

Respiratory distress at birth

Patient Data

Age: 1 day
Gender: Male
X-ray

Day 1 of life

The right hemithorax is expanded by a cystic mass lesion with mediastinal shift to the left.

X-ray

10 months later

10 months later the child has similar appearances to the previous imaging with a hyper-expanded right lung and mediastinal shift.

There is regional hyperinflation on the right which is not confined to one lobe or segment. Vascularity is normal.

Case Discussion

Regional right-sided hyperinflation is not confined to a lobe or segment and crosses fissural boundaries. The vascularity of both lungs appears normal.

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Case information

rID: 22542
Case created: 6th Apr 2013
Last edited: 2nd Mar 2017
Systems: Paediatrics, Chest
Inclusion in quiz mode: Included

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