Mauclaire disease is a rare disease and refers to avascular necrosis of the metacarpal heads, which usually appears between ages of 13 and 18 years. This condition may lead to early closure of epiphyseal growth plate and growth disturbance of the involved finger.
The aetiology is controversial. Few reports describe the association with trauma, steroid use and systemic lupus erythematosus.
Localized pain, swelling and restricted range of motion in the affected metacarpophalengeal joint are the main clinical presentations.
In plain radiography of the hand flattening of the metacarpal heads , widening of the joint space and signs of deforming osteoarthritis may seen at initial images.
Osteochondral fragments and periostitis with cortical thickening of the metaphyses are characteristic.
History and etymology
It was first described by Mauclaire in 1927.
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