von Hippel Lindau

Case contributed by Frank Gaillard
Diagnosis certain
  • Note: This case has been tagged as "legacy" as it no longer meets image preparation and/or other case publication guidelines.
mri
Sagittal
T1 C+
This study is a stack
Axial
T2
Download
Info

Selected MRI images demonstrate multiple enhancing intramedullary lesions, the largest at C4/5, with an associated syrinx. 

dsa
This study is a stack
Frontal
Vertebral artery
Lateral
Vertebral artery
Download
Info

Catheter angiography demonstrates the cord lesions to be very hypervascular consistent with hemangioblastoma. 

mri
Coronal T1
C+ fat sat
Coronal
T2
Axial
T2
Download
Info

MRI demonstrates a left inferior pole renal mass consistent with a renal cell carcinoma. 

Case Discussion

This individual has established von Hippel Lindau disease with a renal cell cancer on the left and cervical cord hemangioblastomas with an associated syrinx.

How to use cases

You can use Radiopaedia cases in a variety of ways to help you learn and teach.

Creating your own cases is easy.

:

Updating… Please wait.

 Unable to process the form. Check for errors and try again.

 Thank you for updating your details.