Presentation
Known case of congenital heart disease, now with haemoptysis.
Patient Data
The right pulmonary artery originates from the ascending aorta. The left pulmonary artery continues directly from the main pulmonary artery, displaying the “moustache sign." A patent ductus arteriosus is also noted.
The right lower lobe displays patchy consolidation with peripheral ground-glass opacities, known as "halo sign," most likely indicating pulmonary haemorrhage. The right lung exhibits venous congestion with dilated pulmonary veins.
Case Discussion
Anomalous origin of the right or left pulmonary artery from the aorta is a rare form of congenital heart disease affecting considerably less than 1%. Due to high-flow and high-pressure left-to-right shunt physiology, this condition can lead to pulmonary arterial hypertension.
Unfortunately, there is a high mortality rate in the first few months after birth, which is why early diagnosis and treatment are so important and why surgical intervention is often required during the perinatal period.
The more common subtype of this condition is the anomalous origin of the right pulmonary artery (>80% of cases) is commonly associated with patent ductus arteriosus in contrast to the anomalous origins of the left pulmonary artery 1.
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