Congenital cystic adenomatoid malformation (CCAM)

Case contributed by Frank Gaillard
Diagnosis almost certain


Respiratory distress

Patient Data

Age: Neonate
  • Note: This case has been tagged as "legacy" as it no longer meets image preparation and/or other case publication guidelines.

Multiloculated cystic lesion in right hemithorax with marked mediastinal shift to the left.

There is a large multiloculated cystic mass centered in the right lower lobe. The multiloculations are typical for a congenital cystic adenomatoid malformation. The periphery of the lesion shows some wall thickening and ill-defined infiltration into the surrounding parenchyma which raises the possibility of some intercurrent inflammation or infection.The cystic mass appears to arise largely from the apical segment of the right lower lobe. The posterior medial segment shows quite striking congestion and is suggestive of impaired lymphatic drainage from this segment. There is hyperinflation of the basal medial and basal lateral segment. The anterior basal segment of the lower lobe appears to have reasonably normal parenchyma. The mass effect of the cystic lesion displaces the posterior right upper lobe superiorly and displaces the hilar and the right middle lobe anteriorly.

The left lung appears normal.

Case Discussion

Congenital cystic adenomatoid malformation (also known as congenital pulmonary airways malformation) diagnosed antenataly shown here in a neonate.

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