Citation, DOI, disclosures and article data
Citation:
Ibrahim D, Deng F, Smith H, Infantile fibrosarcoma of the lung. Reference article, Radiopaedia.org (Accessed on 05 Dec 2024) https://doi.org/10.53347/rID-64464
Infantile fibrosarcoma of the lung, also known as primary bronchopulmonary fibrosarcoma, is a very rare spindle-cell tumor.
Epidemiology
More than 80% of cases are reported to occur within the 1st year of life. There is a slight predominance in male infants 1,2.
Clinical presentation
Patients may present with respiratory symptoms, fever, anemia and hypoglycemia.
Radiographic features
The imaging features of infantile fibrosarcoma, specifically in the lung, have not been described. However, extrapulmonary tumors on MRI tend to be hyperintense on T1 and T2 weighted sequences and demonstrate heterogeneous enhancement associated with tumoral hemorrhage 3.
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1. Lichtenberger JP, Biko DM, Carter BW, Pavio MA, Huppmann AR, Chung EM. Primary Lung Tumors in Children: Radiologic-Pathologic Correlation From the Radiologic Pathology Archives. (2018) Radiographics : a review publication of the Radiological Society of North America, Inc. 38 (7): 2151-2172. doi:10.1148/rg.2018180192 - Pubmed
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2. Corsi A, Boidrini R, Bosnian C. Congenital-Infantile Fibrosarcoma: Study of Two Cases and Review of the Literature:. (2018) Tumori Journal. 5 (5): 371. doi:10.1177/1756283X10363751 - Pubmed
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3. Ainsworth KE, Chavhan GB, Gupta AA, Hopyan S, Taylor G. Congenital infantile fibrosarcoma: review of imaging features. (2014) Pediatric radiology. 44 (9): 1124-9. doi:10.1007/s00247-014-2957-5 - Pubmed
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