Lie classification of vasculitis

The Lie classification of vasculitis was proposed in 1994. 

Classification

Primary vasculitides

• affecting large, medium, and small blood vessels (see large vessel vasculitides)
  • Takayasu arteritis
  • temporal arteritis (giant cell arteritis)
  • isolated angiitis of the central nervous system
  • Hughes-Stovin syndrome
• affecting medium and small blood vessels
  • polyarteritis nodosa (PAN)
  • Churg-Strauss syndrome
  • Wegener granulomatosis
• affecting small vessels
  • microscopic polyangiitis(microscopic polyarteritis)
  • Henoch-Schönlein purpura
  • cutaneous leukocytoclastic angiitis
  • idiopathic, pauci-immune pulmonary capillaritis (IPIPC)
• miscellaneous conditions
  • Buerger disease: thrombangitis obliterans
  • Cogan syndrome
  • Kawasaki disease
  • Goodpasture syndrome
  • Behcet syndrome

Secondary vasculitides

• infection related-related vasculitis
• vasculitis secondary to connective tissue disease, e.g. SLE, rheumatoid arthritis
• drug hypersensitivity related vasculitis
• vasculitis secondary to mixed essential cryoglobulinemia - cryoglobulinaemic vasculitis
• malignancy related-related vasculitis (usually lympho proliferativelymphoproliferative types)
• hypocomplementemic urticaria vasculitis
• post organ transplant vasculitis
• pseudovasculitic syndromes
  • myxoma
  • endocarditis
  • Sneddon syndrome

See also

• vasculitis
• revised international chapel hill consensus conference nomenclature of vasculitides