GOOD NEWS: We have fixed the DICOM uploading problem. New cases should work fine. More info radiopaedia.org/chat

Hemangioblastoma: von Hippel-Lindau syndrome

Case contributed by Frank Gaillard
Diagnosis certain

Patient Data

Age: Young adult
Gender: Male

Note: This case has been tagged as "legacy" as it no longer meets image preparation and/or other case publication guidelines.

Cystic lesion with non enhancing walls and vividly enhancing mural nodule in cerebellum: hemangioblastoma

Case Discussion

Final Diagnosis:

Cerebellum: Hemangioblastoma (clinical history of von Hippel-Lindau syndrome).

Microscopic Description:

Sections show the specimen to consist of a vascular tumor associated with small portions of cerebellar tissue. The tumor is characterized by a capillary component, large ectatic vascular structures and cystic elements containing proteinaceous fluid. These structures are within a stromal tumor background composed of clear cells with small round nuclei. In areas, focal permeation into cerebellar tissue is observed.

How to use cases

You can use Radiopaedia cases in a variety of ways to help you learn and teach.

Creating your own cases is easy.

Updating… Please wait.

 Unable to process the form. Check for errors and try again.

 Thank you for updating your details.