Rhabdomyosarcomas (head and neck)
Rhabdomyosarcomas of the head and neck represent a large proportion (~40%) of all rhabdomyosarcomas. For a general discussion of this tumour, please refer to rhabdomyosarcoma.
There are usually of the embryonal in cell subtype and are essentially only seen in children. They are classified by location into:
- orbital rhabdomyosarcoma: good prognosis (90% long term survival)
- para-meningeal rhabdomyosarcoma: worse prognosis (50% long term survival)
- other head and neck locations
Middle ear rhabdomyosarcomas are rare, accounting for only 7% of head and neck rhabdomyosarcomas. They typically present similarly to chronic otomastoiditis and are usually diagnosed too late for curative treatment. Frequently (30%) cranial nerve involvement is present at the time of diagnosis.
- 1. Schepper AM, Parizel PM, Vanhoenacker FM. Imaging of soft tissue tumors. Springer Verlag. (2006) ISBN:3540248099. Read it at Google Books - Find it at Amazon
- 2. Swartz JD, Loevner LA. Imaging of the Temporal Bone. Thieme Medical Pub. (2008) ISBN:1588903451. Read it at Google Books - Find it at Amazon