Cystic fibrosis
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Diagnosis almost certain
Presentation
Pre-operative assessment.
Patient Data
Age: 25 years
Gender: Female
From the case:
Cystic fibrosis
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Severe bilateral central bronchiectasis. Left subclavian chest port.
From the case:
Cystic fibrosis
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Bilateral severe, widespread bronchiectasis with occasional mucus plugging and background mosaic attenuation, most likely due to air trapping. Lung volumes are increased.
Case Discussion
A case of advanced cystic fibrosis. This imaging was obtained shortly before bilateral lung transplantation.