Restrictive cardiomyopathy

Restrictive cardiomyopathy is the least common subtype of cardiomyopathy that is characterised by a marked decrease in ventricular compliance. 

Patients can present with symptoms and signs of left ventricular failure and/or right ventricular failure 9

It is predominantly a disease of diastolic dysfunction where the systolic (contractile) of the myocardium is usually unaffected. 

Aetiology

Recognised causes which can give a restrictive type pattern include:

Plain radiograph

The heart size can be normal. Sometimes there may be evidence of biatrial dilatation.

Echocardiography

It shows diastolic dysfunction.

MRI

Cardiac MRI is useful for differentiating between constrictive pericarditis. May show biatrial enlargement with minimal or no ventricular enlargement. Cine MRI will show altered diastolic filling. 

Share article

Article information

rID: 8007
System: Cardiac
Section: Gamuts
Tag: cases
Synonyms or Alternate Spellings:
  • Restrictive cardiomyopathy
  • Restrictive cardiomyopathies

Support Radiopaedia and see fewer ads

Cases and figures

  • Drag
    Case 1: with cardiac amyoidosis
    Drag here to reorder.
  • Updating… Please wait.
    Loadinganimation

    Alert accept

    Error Unable to process the form. Check for errors and try again.

    Alert accept Thank you for updating your details.