External auditory canal cholesteatoma
Updates to Article Attributes
External areturnsauditory canal cholesteatomas are uncommon locations (EACCs) are rare, the external auditory canal being an unusual site for cholesteatomascholesteatoma, which are usually in the middle ear or petrous apex. When they occur lateral to the tympanic membrane, they are referred to as external auditory canal cholesteatomas.
Epidemiology
The external acoustic canal is a rare location for a cholesteatoma with an estimated incidence around 1.2 per 1,000 new otological patients. The overall incidence rate in one large study was 0.30 per year per 100,000 inhabitants 1. For comparison, the annual incidence of middle ear cholesteatoma is around 9.2 per 100,000.
Pathology
A distinction from keratosis obturanshas been introduced only in the last few decades. Both mainly consist of epithelial debris in the external acoustic canal. The most useful findings confirming an external auditory canal cholesteatoma are focal osteonecrosis with or without sequestration and lack of epithelial covering of the bony surface 2. The distinction between keratosis obliterans and cholesteatomas is not merely one of pedantry, but impacts on treatment strategy 3.
Classification
External auditory canal cholesteatoma can be divided into:
-
primary (idiopathic/spontaneous)
- rare
- no antecedent cause identified
-
secondary
- more common
- postoperative, postinflammatory, posttraumatic, radiation-induced
A special type of secondary cholesteatoma of the external auditory canal which is worth mentioning separately are those associated with congenital atresia of the external auditory canal.
Radiographic features
Plain filmradiograph
The Schüller, Stenvers, and Mayer views of the petrous bone have been largely replaced by CT.
CT
High-resolution bone window temporal bone CT is the method of choice to localise the lesioncholesteatoma and to demonstrate bony erosions. They appear as soft tissue attenuating lesions.
MRI
CannotMRI cannot show the early involvement of compact bone. Its role in EACC is unknownnot defined.
Treatment and prognosis
Small lesions can be treated endoscopically under local anaesthesia, whereas larger lesions need surgery to remove the cholesteatoma and affected bone areas. Grafting of defects may be necessary. Prognosis depends on the extent at the time of diagnosis.
History and etymology
External auditory canal cholesteatomas were first reported by Toynbee in 1850.
Differential diagnosis
General imaging differential considerations include
-<p><strong>External areturns canal cholesteatomas</strong> are uncommon locations for <a href="/articles/cholesteatoma">cholesteatomas</a>, which are usually in the <a href="/articles/middle-ear">middle ear</a> or <a href="/articles/petrous-apex">petrous apex</a>. When they occur lateral to the <a href="/articles/tympanic-membrane">tympanic membrane</a>, they are referred to as <a href="/articles/external-auditory-canal">external auditory canal</a> cholesteatomas. </p><h4>Epidemiology</h4><p>The external acoustic canal is a rare location for a cholesteatoma with an estimated incidence around 1.2 per 1,000 new otological patients. The overall incidence rate in one large study was 0.30 per year per 100,000 inhabitants <sup>1</sup>. For comparison, the annual incidence of middle ear cholesteatoma is around 9.2 per 100,000.</p><h4>Pathology</h4><p>A distinction from <a title="Keratosis obturans" href="/articles/keratosis-obturans">keratosis obturans</a><a href="/articles/keratosis-obturans"> </a>has been introduced only in the last few decades. Both mainly consist of epithelial debris in the external acoustic canal. The most useful findings confirming an external auditory canal cholesteatoma are focal osteonecrosis with or without sequestration and lack of epithelial covering of the bony surface <sup>2</sup>. The distinction between keratosis obliterans and cholesteatomas is not merely one of pedantry, but impacts on treatment strategy <sup>3</sup>.</p><h5>Classification</h5><p>External auditory canal cholesteatoma can be divided into:</p><ul>- +<p><strong>External auditory canal cholesteatomas</strong> (<strong>EACCs</strong>) are rare, the <a title="External auditory canal" href="/articles/external-auditory-canal">external auditory canal</a> being an unusual site for <a href="/articles/cholesteatoma">cholesteatoma</a>, which are usually in the <a href="/articles/middle-ear">middle ear</a> or <a href="/articles/petrous-apex">petrous apex</a>. </p><h4>Epidemiology</h4><p>The external acoustic canal is a rare location for a cholesteatoma with an estimated incidence around 1.2 per 1,000 new otological patients. The overall incidence rate in one large study was 0.30 per year per 100,000 inhabitants <sup>1</sup>. For comparison, the annual incidence of middle ear cholesteatoma is around 9.2 per 100,000.</p><h4>Pathology</h4><p>A distinction from <a href="/articles/keratosis-obturans">keratosis obturans</a><a href="/articles/keratosis-obturans"> </a>has been introduced only in the last few decades. Both mainly consist of epithelial debris in the external acoustic canal. The most useful findings confirming an external auditory canal cholesteatoma are focal osteonecrosis with or without sequestration and lack of epithelial covering of the bony surface <sup>2</sup>. The distinction between keratosis obliterans and cholesteatomas is not merely one of pedantry, but impacts on treatment strategy <sup>3</sup>.</p><h5>Classification</h5><p>External auditory canal cholesteatoma can be divided into:</p><ul>
-</ul><p>A special type of secondary cholesteatoma of the external auditory canal which is worth mentioning separately are those associated with <a href="/articles/external-auditory-canal-atresia">congenital atresia of the external auditory canal</a>.</p><h4>Radiographic features</h4><h5>Plain film</h5><p><a href="/articles/sch-ller-view">Schüller</a>, <a href="/articles/stenvers-view">Stenvers</a>, and <a href="/articles/mayer-view">Mayer views</a> of the petrous bone have been largely replaced by CT.</p><h5>CT</h5><p>High-resolution bone window CT is the method of choice to localise the lesion and to demonstrate bony erosions. They appear as soft tissue attenuating lesions. </p><h5>MRI</h5><p>Cannot show the early involvement of compact bone. Its role in EACC is unknown.</p><h4>Treatment and prognosis</h4><p>Small lesions can be treated endoscopically under local anaesthesia, whereas larger lesions need surgery to remove the cholesteatoma and affected bone areas. Grafting of defects may be necessary. Prognosis depends on the extent at the time of diagnosis.</p><h4>History and etymology</h4><p>External auditory canal cholesteatomas were first reported by <strong>Toynbee</strong> in 1850.</p><h4>Differential diagnosis</h4><p>General imaging differential considerations include</p><ul>- +</ul><p>A special type of secondary cholesteatoma of the external auditory canal which is worth mentioning separately are those associated with <a href="/articles/external-auditory-canal-atresia">congenital atresia of the external auditory canal</a>.</p><h4>Radiographic features</h4><h5>Plain radiograph</h5><p>The <a href="/articles/sch-ller-view">Schüller</a>, <a href="/articles/stenvers-view">Stenvers</a>, and <a href="/articles/mayer-view">Mayer views</a> of the petrous bone have been largely replaced by CT.</p><h5>CT</h5><p>High-resolution bone window <a title="temporal bone CT" href="/articles/temporal-bone-ct">temporal bone CT</a> is the method of choice to localise the cholesteatoma and to demonstrate bony erosions. They appear as soft tissue attenuating lesions. </p><h5>MRI</h5><p>MRI cannot show the early involvement of compact bone. Its role in EACC is not defined.</p><h4>Treatment and prognosis</h4><p>Small lesions can be treated endoscopically under local anaesthesia, whereas larger lesions need surgery to remove the cholesteatoma and affected bone areas. Grafting of defects may be necessary. Prognosis depends on the extent at the time of diagnosis.</p><h4>History and etymology</h4><p>External auditory canal cholesteatomas were first reported by <strong>Toynbee</strong> in 1850.</p><h4>Differential diagnosis</h4><p>General imaging differential considerations include</p><ul>