Adamantinomatous craniopharyngioma

intraIntra and supra sellar mass measuring 3cm in its largest axis and compresses the optic chiasm is hypointense on T1 and hyperintense on T2 ( predominantly cystic component with mural nodule ) .

afterAfter contrast demonstrates a suprasellar predominantly cystic mass with peripheral enhancement.

Start the patient with headache, and body treatments received by this reason for one year without improvement, adding visual symptomatology, subsequently referred to our service to imaging study.

Craniopharyngioma is the third of the three pathologies derived from Rathke's cleft epithelium. Technically these are benign tumors, but unlike Rathke's cleft cysts, they have thick walls and are locally invasive.

Macroscopically, it is a complex mass with multiple nodules at the base of the brain, sinuating along the fissures. Often, it can not be completely resected.

The estimated incidence is 1.4 cases per million children per year. Overall, craniopharyngioma accounts for 1-3% of intracranial tumors and 13% of suprasellar tumors. In children, craniopharyngioma represents 5-10% of all tumors and 56% of sellar and suprasellar tumors. No definite genetic relationship has been found, and very few familial cases have been reported.

Higher frequencies of all intracranial tumors have been reported from Africa, the Far East, and Japan; they are 18%, 16%, and 10.5%, respectively.

A slight male predominance exists in all age groups (55%). Craniopharyngiomas have a bimodal age distribution pattern, with a peak between ages 5 and 14 years and in adults older than 65 years, although there reports involving all age groups.