Presentation
Progressive yellowish discolouration of the eyes, urine, and skin all over the body.
Patient Data
On MRCP sequence:
hypoplastic gallbladder with an average length measuring 1.2 x 0.8 cm (normal length >19 mm) with hepatomegaly
non-visualization of the common hepatic duct, common bile duct, and intrahepatic duct
with increased periportal echogenicity is noted. overall features consistent with congenital biliary atresia (type 3 Kasai)
Case Discussion
Biliary atresia is a congenital anomaly in which there is a variable degree of atresia of the extrahepatic biliary ducts. with an incidence of approximately 1:15000 having male prediction.
A baby with congenital atresia is normal at birth, with symptoms starting to develop after 2 weeks to 2 months of age. Less than 10% of cases present with syndromic conditions such as polysplenia, interrupted IVC, etc.
In this case, the gall bladder is hypoplastic with a length of less than 19 mm, with non-visualization of the common hepatic duct and common bile duct, and increased periportal signal intensity along with hepatomegaly. Overall features are consistent with biliary atresia Kasai type 3.
Unable to process the form. Check for errors and try again.