Hypothalamic hamartoma
Updates to Case Attributes
Hypothalamic hamartoma is a relatively rare congenital lesion consisting of non-neoplastic heterotrophic grey and white matter with a varying degree of differentiation. It occurs at the tubercinerumtuber cinereum of the hypothalamus on the floor of the third ventricle.
The patients usually present with precocious puberty, accelerated growth, gelastic seizures, behavioural abnormalities etc. Our patient presented with precocious puberty and increased body height but no seizures.
Contributed by Dr. Aruna Pallewatte and Dr. Umakanthan Nadaraja
-<p><a href="/articles/hypothalamic-hamartoma" title="Hypothalamic hamartoma">Hypothalamic hamartoma</a> is a relatively rare congenital lesion consisting of non-neoplastic heterotrophic grey and white matter with a varying degree of differentiation. It occurs at the tubercinerum of the hypothalamus on the floor of the third ventricle.</p><p>The patients usually present with precocious puberty, accelerated growth, gelastic seizures, behavioural abnormalities etc. Our patient presented with precocious puberty and increased body height but no seizures. </p><p>Contributed by Dr. Aruna Pallewatte and Dr. Umakanthan Nadaraja</p>- +<p><a href="/articles/hypothalamic-hamartoma" title="Hypothalamic hamartoma">Hypothalamic hamartoma</a> is a relatively rare congenital lesion consisting of non-neoplastic heterotrophic grey and white matter with a varying degree of differentiation. It occurs at the tuber cinereum of the hypothalamus on the floor of the third ventricle.</p><p>The patients usually present with precocious puberty, accelerated growth, gelastic seizures, behavioural abnormalities etc. Our patient presented with precocious puberty and increased body height but no seizures. </p><p>Contributed by Dr. Aruna Pallewatte and Dr. Umakanthan Nadaraja</p>
References changed:
- 1. Baheti N, Cherian A, Menon R, Radhakrishnan A. Teaching Video NeuroImages: Hypothalamic Hamartoma: An Overlooked Entity. Neurology. 2011;76(6):e26. <a href="https://doi.org/10.1212/wnl.0b013e31820b761a">doi:10.1212/wnl.0b013e31820b761a</a> - <a href="https://www.ncbi.nlm.nih.gov/pubmed/21300965">Pubmed</a>
- 1. Baheti N, Cherian A, Menon R, Radhakrishnan A. Teaching Video NeuroImages: Hypothalamic Hamartoma: An Overlooked Entity. Neurology. 2011;76(6):e26. <a href="https://doi.org/10.1212/wnl.0b013e31820b761a">doi:10.1212/wnl.0b013e31820b761a</a> - <a href="https://www.ncbi.nlm.nih.gov/pubmed/21300965">Pubmed</a>
- 2. Smith J. Parasellar Tumors. Top Magn Reson Imaging. 2005;16(4):307-15. <a href="https://doi.org/10.1097/01.rmr.0000224687.29371.9a">doi:10.1097/01.rmr.0000224687.29371.9a</a> - <a href="https://www.ncbi.nlm.nih.gov/pubmed/16785846">Pubmed</a>
- 2. Smith JK. Parasellar Tumors: Suprasellar and Cavernous Sinuses. Topics in Magnetic Resonance Imaging.2005;16 - 4:307-315.
- Baheti N, Cherian A, Menon R, Radhakrishnan A. Teaching Video NeuroImages: Hypothalamic Hamartoma: An Overlooked Entity. Neurology. 2011;76(6):e26. <a href="https://doi.org/10.1212/wnl.0b013e31820b761a">doi:10.1212/wnl.0b013e31820b761a</a> - <a href="https://www.ncbi.nlm.nih.gov/pubmed/21300965">Pubmed</a>
- 1. Baheti NN, Cherian A, Menon R. Hypothalamic hamartoma: An overlooked entity.Neurology.2011;76;e26
Tags changed:
- legacy
- legacy case
Updates to Study Attributes
A well-defined midline lesion in the suprasellar region projecting into the suprasellar cistern. It shows iso signal intensity in T1 weighted images and slightly heterogeneously high signal in T2W and FLAIR images. No significant post-contrast enhancement. Grey white-white differentiation of the cerebral hemisphere is normal.No. No grey matter heterotopia or microgyria. The Corpus callosum and pituitary gland are normal.
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