Presentation
Left exophthalmos
Patient Data
The MRI sequences demonstrate a left axial proptosis grade 2 with poorly marginated, multiloculated orbital cystic mass of intra and extraconal location of intermediate signal on T1 with areas of high signal, and heterogeneous high signal T2 with multiple fluid-fluid levels well-visualized on axial and coronal T2 fat sat sequences, corresponding to hemorrhagic, lymphatic, or proteinaceous content within the cystic spaces. The postcontrast sequences reveal a heterogeneous enhancement mainly of the margins of the cystic spaces.
Case Discussion
MRI features characteristic of an orbital lymphatic malformation.
Orbital lymphatic malformation is considered as a congenital benign vascular malformation with variable lymphatic and venous components.
The differential diagnosis should include mainly: