Presentation
Cough and SOB since contracting COVID-19 two years prior. Evaluate for lung pathology.
Patient Data
No previous imaging available for comparison.
Curvilinear tubular opacity overlying the right mid to lower zone.
Loss of the right heart border.
Reduced right lung volume.
Imaging features are in keeping with scimitar syndrome.
Partial anomalous venous drainage identified with all right sided pulmonary veins draining to the IVC, resulting in a volume-loaded right heart from a significant shunt.
There is dextroposition of the heart due to right lung hypoplasia. There is no evidence of an associated ASD. The left ventricle is of normal size and systolic function.
The right ventricle is dilated and of normal systolic function.
Mild-moderate functional tricuspid regurgitation.
Findings are consistent with scimitar syndrome.
Case Discussion
Imaging features above are in keeping with scimitar syndrome. In this instance, it was the patient's first presentation and this was discovered incidentally.
Scimitar syndrome, also known as hypogenetic lung syndrome, is characterized by a hypoplastic lung that is drained by an anomalous pulmonary vein into the systemic venous system. It is a type of partial anomalous pulmonary venous return and is one of the several findings in congenital pulmonary venolobar syndrome.
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