Sphenoid wing dysplasia

Case contributed by Dalia Ibrahim , 27 Feb 2017
Diagnosis certain
Changed by Yusra Sheikh, 5 Jan 2021

Updates to Case Attributes

Age changed from 20-year-old to 20 years.

Systems changed:

  • Musculoskeletal

Updates to Study Attributes

Findings was changed:

Absence of the right sphenoid wing and the lateral orbital wall. Consequently the right temporal lobe with the surrounding CSF and enlarged arachnoid space are prolapsing into the right orbit producing distorsion of the optic nerve and subsequent proptosis.

A gappinggaping bony defect is seen in the posterior aspect of the right orbit giving the "Empty"empty orbit sign"

Absent anatomical landmarks of the optic nerve canal,anterior, anterior clinoid, superior and inferior orbital fissures.

Right upper eyelid subcutaneous soft tissue thickening, likely representing plexiform neurofibromatosis.

Diffuse atrophic changes of the right cerebral hemisphere.

Cortical irregularity of the right orbital roof and parietal bone secondary to old trauma and surgical intervention.

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