Presentation
Epilepsy with developmental delay
Patient Data
Age: 15 years
Gender: Female
From the case:
Sturge-Weber syndrome
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Left parietooccipital cortical calcification with a tram track appearance.
Ipsilateral left occipital horn choroid plexus enlargement.
Case Discussion
Sturge-Weber syndrome (encephalotrigeminal angiomatosis) is a phakomatosis characterized by a facial port-wine birthmark (capillary malformation) and pial angiomas.
CT findings:
subcortical calcification and associated parenchymal volume loss
tram-track sign of cortical and subcortical calcification
calvarial and regional sinus enlargement may be evident
ipsilateral choroid plexus may be enlarged
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