3 results found
Article
Haemorrhagic shock and encephalopathy syndrome
Haemorrhagic shock and encephalopathy syndrome (HSES) is a rare paediatric encephalopathy syndrome with a high mortality rate.
Epidemiology
Haemorrhagic shock and encephalopathy syndrome is considered rare, although the exact global incidence and prevalence is not known. The condition occurs i...
Article
Langerhans cell histiocytosis (CNS manifestations)
The central nervous system (CNS) is an uncommonly involved organ system in Langerhans cell histiocytosis (LCH). Involvement of the CNS is related but distinct from involvement of the skull or craniofacial structures, which are discussed separately in the article skeletal manifestations of LCH. F...
Article
Sickle cell disease
Sickle cell disease (SCD) (historically also known as drepanocytosis) is a hereditary (autosomal recessive) condition resulting in the formation of abnormal haemoglobin (a haemoglobinopathy), which manifests as multisystem ischaemia and infarction, as well as haemolytic anaemia.
Haemoglobin SC...