Urethral duplication

Changed by Youness Et-tahir, 30 Apr 2022

Updates to Article Attributes

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Urethral duplication is a rare condition in which either a part of the entire urethra is duplicated. It usually occurs in the sagittal plane and the more dorsal copy is usually the duplication.

Pathology

A urethral duplication may occur due to a variety of developmental miscues. In a woman, it is thought to arise from delayed fusion of the Mullerian ducts and urogenital sinus 2

Radiographic features

In malesExploration of urethral duplication could be done by retrograde urethrography and voiding cystourethrography which are considered the main diagnosis procedures, a partial or complete duplicationeven by sonourethrography and MRI.

Retrograde urethrography and voiding cystourethrography visualise the size, shape and position of the urethra can be seen with urethographytwo channels.

In addition to the evaluation of duplicated urethras, MRI explores periurethral tissues and associated genitourinary abnormalities. In

In males, two separate meatuses withEffman classification is the abilitymost used system to void through bothdistinguish the several types of urethral duplication. The type IIA2 is a morethe most common configurationone.

Possible duplication of the female urethra is better studied with MRI.  Two high signal-intensity central spots may be apparent on an axial view of the pelvis in the region of the urethra.

Treatment and prognosis

A small retrospective study (n=20) found the use of both buccal and urinary bladder mucosa for urethral repair have good results and that Y-type urethral duplication is most difficult to repair surgically 5.

Differential diagnosis

In a male, hypospadias can be considered (glanular dimple not patent).

See also

Congenital anomalies of the male urethra

Effman classification

  • -<p><strong>Urethral duplication </strong>is a rare condition in which either a part of the entire urethra is duplicated. It usually occurs in the sagittal plane and the more dorsal copy is usually the duplication.</p><h4>Pathology</h4><p>A urethral duplication may occur due to a variety of developmental miscues. In a woman, it is thought to arise from delayed fusion of the Mullerian ducts and urogenital sinus <sup>2</sup>. </p><h4>Radiographic features</h4><p>In males, a partial or complete duplication of the urethra can be seen with urethography. In males, two separate meatuses with the ability to void through both is a more common configuration.</p><p>Possible duplication of the female urethra is better studied with MRI.  Two high signal-intensity central spots may be apparent on an axial view of the pelvis in the region of the urethra.</p><h4>Treatment and prognosis</h4><p>A small retrospective study (n=20) found the use of both buccal and urinary bladder mucosa for urethral repair have good results and that Y-type urethral duplication is most difficult to repair surgically <sup>5</sup>.</p><h4>Differential diagnosis</h4><p>In a male, <a href="/articles/hypospadias">hypospadias</a> can be considered (glanular dimple not patent).</p>
  • +<p><strong>Urethral duplication </strong>is a rare condition in which either a part of the entire urethra is duplicated. It usually occurs in the sagittal plane and the more dorsal copy is usually the duplication.</p><h4>Pathology</h4><p>A urethral duplication may occur due to a variety of developmental miscues. In a woman, it is thought to arise from delayed fusion of the Mullerian ducts and urogenital sinus <sup>2</sup>. </p><h4>Radiographic features</h4><p>Exploration of urethral duplication could be done by retrograde urethrography and voiding cystourethrography which are considered the main diagnosis procedures, or even by sonourethrography and MRI.</p><p>Retrograde urethrography and voiding cystourethrography visualise the size, shape and position of the two channels.</p><p>In addition to the evaluation of duplicated urethras, MRI explores periurethral tissues and associated genitourinary abnormalities.</p><p>In males, <a href="/articles/effman-classification-of-urethral-duplication">Effman classification</a> is the most used system to distinguish the several types of urethral duplication. The type IIA2 is the most common one.</p><p>Possible duplication of the female urethra is better studied with MRI.  Two high signal-intensity central spots may be apparent on an axial view of the pelvis in the region of the urethra.</p><h4>Treatment and prognosis</h4><p>A small retrospective study (n=20) found the use of both buccal and urinary bladder mucosa for urethral repair have good results and that Y-type urethral duplication is most difficult to repair surgically <sup>5</sup>.</p><h4>Differential diagnosis</h4><p>In a male, <a href="/articles/hypospadias">hypospadias</a> can be considered (glanular dimple not patent).</p><h4>See also</h4><p><a title="Congenital anomalies of the male urethra" href="/articles/congenital-anomalies-of-the-male-urethra">Congenital anomalies of the male urethra</a></p><p><a title="Effman Classification of urethral duplication" href="/articles/effman-classification-of-urethral-duplication">Effman classification</a></p>

References changed:

  • 6. Bhadury S, Parashari U, Singh R, Kohli N. MRI in Congenital Duplication of Urethra. Indian Journal of Radiology and Imaging. 2009;19(03):232-4. <a href="https://doi.org/10.4103/0971-3026.54884">doi:10.4103/0971-3026.54884</a> - <a href="https://www.ncbi.nlm.nih.gov/pubmed/19881093">Pubmed</a>
  • 7. Guglielmetti L, Delcont M, Walker J, Wilcox D, Vuille-dit-Bille R. Urethral Duplication—Epidemiology, Diagnosis, and Treatment in a Case Series of 19 Patients. J Pediatr Urol. 2020;16(3):385.e1-9. <a href="https://doi.org/10.1016/j.jpurol.2020.02.010">doi:10.1016/j.jpurol.2020.02.010</a> - <a href="https://www.ncbi.nlm.nih.gov/pubmed/32197934">Pubmed</a>

Systems changed:

  • Paediatrics

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