Presentation
Chronic cough and dyspnea
Patient Data
Lower lobe predominant fibrosis with marked volume loss, ground-glass opacity, peribronchovascular reticular opacity and traction bronchiectasis extending from the lung bases towards the hila. Minor honeycombing. Extensive subpleural reticulation. Small irregular opacity at the right lung apex.
The esophagus is dilated throughout its length.
Bilateral glenohumeral joint arthropathy with periarticular calcifications.
Upper abdominal images show dilated colonic loops loaded with fecal matter.
Case Discussion
The constellation of findings is suggestive of scleroderma (systemic sclerosis) with respiratory, musculoskeletal and GIT manifestations.