Atypical choroid plexus papilloma

Case contributed by Sepehr Haghighi
Diagnosis certain

Presentation

A patient with severe headache and intractable vomiting

Patient Data

Age: 2 years
Gender: Male

A frond-like isosignal T1W/T2W intraventricular mass within the 4th ventricle without invasion to cerebellar hemispheres shows marked enhancement following contrast administration. Extension of mass into magendie foramen is seen.

Obstructive hydrocephalus is visible by this mentioned mass associated with periventricular interstitial edema.

Compression of mass on the dorsal aspect of the brain stem is visible.

No DWI restriction is identified.

pathology

Case Discussion

Atypical choroid plexus papillomas are WHO grade 2 tumors derived from choroid plexus epithelium with intermediate clinical and pathological features between more indolent choroid plexus papillomas and more aggressive choroid plexus carcinomas.

The differential is essentially that of other choroid plexus tumors:

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