Congenital diaphragmatic hernia

Case contributed by Dr Tim Luijkx

Presentation

Respiratory distress immediately after birth, pulmonary hypertension. Intubated.

Patient Data

Age: 1 day
Gender: Female
X-ray

Large diaphragmatic hernia with intrathoracic herniation of intestines and part of liver, as demonstrated by intrathoracic position of venous umbilical catheter. Mediastinal shift.

Case Discussion

Large congenital diaphragmatic hernia with intrathoracic position of intestines and liver. Right lung turned out to be hypoplastic. 

Operative closure of the diaphragmatic defect. Initially only skin was closed because of a mismatch between abdominal cavity volume and contents, increasing the risk of abdominal compartment syndrome, hence leaving a abdominal wall hernia.

Pulmonary hypertension disappeared. Abdominal wall to be closed later.

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Case information

rID: 32951
Published: 23rd Dec 2014
Last edited: 16th Jul 2018
Inclusion in quiz mode: Included

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