Extraskeletal Ewing sarcoma of the neck
Updates to Case Attributes
Due to the location of the mass and the presence of vascular encasement with splaying of the ICA and ECA, this mass was initially thought to represent a large cervical paraganglioma, either arising from the carotid body and/or vagus nerve. However, in view of atypical features (no intratumoural haemorrhage and lack of flow voids), a schwannomaschwannoma could not be totally excluded.
She also had imaging features in keeping with left vocal cord palsy (confirmed on scope) and left hypoglossal nerve palsy, which correlates with her presenting symptoms.
The patient went on to have debulking surgery, and histopathology results showed Ewing sarcoma.
Extraskeletal Ewing sarcoma is rare compared to Ewing sarcoma of the bone. They tend to be aggressive, with a high rate of local recurrence and distant metastasis. In this patient, a post-operative PET scan showed no evidence of distant metastases.
-<p>Due to the location of the mass and the presence of vascular encasement with splaying of the ICA and ECA, this mass was initially thought to represent a large cervical <a href="/articles/paragangliomas-of-the-head-and-neck" title="Paragangliomas of the head and neck">paraganglioma</a>, either arising from the carotid body and/or vagus nerve. However, in view of atypical features (no intratumoural haemorrhage and lack of flow voids), a<a href="/articles/vagal-schwannoma" title=" vagal schwannoma"> schwannoma</a> could not be totally excluded.</p><p>She also had imaging features in keeping with left vocal cord palsy (confirmed on scope) and left hypoglossal nerve palsy, which correlates with her presenting symptoms.</p><p>The patient went on to have debulking surgery, and histopathology results showed Ewing sarcoma.</p><p><a href="/articles/extraskeletal-ewing-sarcoma" title="Extraskeletal Ewing sarcoma">Extraskeletal Ewing sarcoma</a> is rare compared to Ewing sarcoma of the bone. They tend to be aggressive, with a high rate of local recurrence and distant metastasis. In this patient, a post-operative PET scan showed no evidence of distant metastases.</p>- +<p>Due to the location of the mass and the presence of vascular encasement with splaying of the ICA and ECA, this mass was initially thought to represent a large cervical <a href="/articles/paragangliomas-of-the-head-and-neck" title="Paragangliomas of the head and neck">paraganglioma</a>, either arising from the carotid body and/or vagus nerve. However, in view of atypical features (no intratumoural haemorrhage and lack of flow voids), a <a href="/articles/vagal-schwannoma" title=" vagal schwannoma">schwannoma</a> could not be totally excluded.</p><p>She also had imaging features in keeping with left vocal cord palsy (confirmed on scope) and left hypoglossal nerve palsy, which correlates with her presenting symptoms.</p><p>The patient went on to have debulking surgery, and histopathology results showed Ewing sarcoma.</p><p><a href="/articles/extraskeletal-ewing-sarcoma" title="Extraskeletal Ewing sarcoma">Extraskeletal Ewing sarcoma</a> is rare compared to Ewing sarcoma of the bone. They tend to be aggressive, with a high rate of local recurrence and distant metastasis. In this patient, a post-operative PET scan showed no evidence of distant metastases.</p>
Updates to Study Attributes
Image CT (C+ late arterial phase) ( update )
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