Adolescent patient presenting with recurrent lower abdominal pain each month. She has regular menstrual cycles and well developed secondary sexual characteristics. Initial ultrasound noted a pelvic cystic lesion with echogenic contents.
Loading Stack -
0 images remaining
Uterine didelphys and the left mullarian duct derivatives are distended with fluid consistent with blood signal intensity. There is ipsilateral kidney agenesis and the contralateral kidney is hypertrophied with normal-appearing contralateral mullarian duct derivatives.
Herlyn-Werner-Wunderlich syndrome encompasses
- uterine didelphys with vaginal septum causing hemivaginal obstruction
- consequent unilateral haematocolpos, hematometra, hemosalpix and occasionally hemoperitoneum
- contralateral Mullerian duct is well developed so that the patient presentation is often vague as there is no amenorrhea.
- ipsilateral renal agenesis with compensatory hypertrophy of the contralateral kidney
This patient underwent resection of the left hemiuterus with improvement of her symptoms.