Presentation
Mayer-Rokitansky-Küster-Hauser syndrome. Exclusion of hydropnephrosis.
Patient Data
Age: 40 years
Gender: Female
{"current_user":null,"step_through_annotations":true,"access":{"can_edit":false,"can_download":true,"can_toggle_annotations":true,"can_feature":false,"can_examine_pipeline_reports":false,"can_pin":false},"extraPropsURL":"/studies/78601/annotated_viewer_json?lang=gb"}
Right pelvic kidney. No signs of hydronephrosis.
Left-sided renal agenesis.
Maldescended ovaries on both sides.
Absence of the uterus and upper 2/3 vagina.
Lobulated liver cyst (segment VI).
Case Discussion
This case shows a Mayer-Rokitansky-Küster-Hauser Syndrome type B:
- absence of the uterus and upper 2/3 of the vagina
- maldescended ovaries