Presentation
Incidental finding on ultrasound exam (not shown).
Patient Data
Age: 6 years
Gender: Male
From the case:
Polysplenia syndrome
{"current_user":null,"step_through_annotations":true,"access":{"can_edit":false,"can_download":true,"can_toggle_annotations":true,"can_feature":false,"can_examine_pipeline_reports":false,"can_pin":false},"extraPropsURL":"/studies/144483/annotated_viewer_json?lang=us"}
CT scan demonstrates:
Interruption of the infrahepatic segment of the IVC with hemiazygos continuation
the right renal vein is drained into the left-sided IVC as well as the left renal vein
The post-hepatic segment of the IVC is present and drains only the hepatic veins into the right atrium
Case Discussion
Polysplenia syndrome, also known as left isomerism, is a type of heterotaxy syndrome where there are multiple spleens congenitally as part of left-sided isomerism. Usually associated with congenital heart disease, malrotation of the abdominal viscera and vascular anomalies (such as intrahepatic IVC interruption with azygos/hemiazygos continuation and preduodenal portal vein)
Unable to process the form. Check for errors and try again.