Pulmonary agenesis

Case contributed by Shimalis Tadasa


Respiratory distress since birth

Patient Data

Age: 1 month
Gender: Female

Case Discussion

The results above reveal congenital right pulmonary agenesis.

Pulmonary agenesis is the entire absence of pulmonary parenchyma, bronchi after bifurcation, and their ancillary arteries. Is an uncommon type of unilateral congenital lung anomaly. Patients typically experience breathing problems as newborns and they almost never go unnoticed until puberty.
Pulmonary agenesis differs from other congenital lung anomalies in that:

  • in pulmonary aplasia, it's common to see small, blind-ending rudimentary bronchus.
  • pulmonary hypoplasia is defined by a decrease in lung size and weight, as well as a lack of development of some lung tissue, despite the presence of bronchi and alveoli.

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