Extraventricular neurocytomas are extremely rare WHO grade II primary CNS neoplasms.
The tumours are of neuronal origin and are similar to the comparatively more common central (usually intraventricular) neurocytomas. They were previously known as cerebral neurocytomas however extraventricular neurocytoma is now the correct term in the WHO classification.
Due to their rarity, most features are derived from case reports.
Lesions tend to be generally circumscribed, complex and sometimes large, complex, and variably enhancing masses. They are often partly or mainly cystic and calcification is not uncommon(>10%). They may or may not be associated with peritumoral oedema.
In most instances they are well-defined, cystic and heterogeneously solid, and involves the deep white matter or cortical gray matter of the cerebral hemispheres.
C+ GAD: solid portions amy show showed varying degrees of enhancement
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