Tricuspid atresia
Updates to Article Attributes
Tricuspid atresia is a cyanotic congenital cardiac anomaly which is characterised by agenesis of the tricuspid valve and right ventricular inlet. There is almost always an obligatory intra-atrial connection through either an ASD or patent foramen ovale (PFO) in order for circulation to be complete 5. A small VSD is often also present. In a proportion of cases they may also be associated with transposition of great arteries (TGA).
Pathology
It results from an unequal atrio-ventricular canal division and the right ventricle is typically very hypoplastic.
Associations
Recognised extra-cardiac associations include:
- right
sided-sided aortic arch - absent spleen: asplenia
Radiographic features
Plain radiograph
Chest radiographic features may vary depending on the presence and extent of a VSD or TGA. May demonstrate decreased pulmonary vascularity (i.e. oligaemic appearance). Cardiac size may be normal or enlarged.
Echocardiography/ultrasound
Usually the 1st line imaging modality in utero. AllowsIt allows direct visualisation of the anomaly.
CT and MRI
Allows direct visualisation of anomaly and may typically show a fatty and/or muscular separation of the right atrium from the right ventricle. Cine MRI can offer functional information in addition to anatomy.
-<li><a href="/articles/right-sided-aortic-arch">right sided aortic arch</a></li>- +<li><a href="/articles/right-sided-aortic-arch">right-sided aortic arch</a></li>
-</ul><h4>Radiographic features</h4><h5>Plain radiograph</h5><p>Chest radiographic features may vary depending on the presence and extent of a <a href="/articles/ventricular-septal-defect-vsd">VSD </a>or <a href="/articles/transposition-of-the-great-arteries">TGA</a>. May demonstrate decreased pulmonary vascularity (i.e. oligaemic appearance). Cardiac size may be normal or enlarged.</p><h5>Echocardiography/ultrasound</h5><p>Usually the 1<sup>st</sup> line imaging modality in utero. Allows direct visualisation of anomaly. </p><h5>CT and MRI</h5><p>Allows direct visualisation of anomaly and may typically show a fatty and/or muscular separation of the right atrium from the right ventricle. Cine MRI can offer functional information in addition to anatomy.</p>- +</ul><h4>Radiographic features</h4><h5>Plain radiograph</h5><p>Chest radiographic features may vary depending on the presence and extent of a <a href="/articles/ventricular-septal-defect-vsd">VSD </a>or <a href="/articles/transposition-of-the-great-arteries">TGA</a>. May demonstrate decreased pulmonary vascularity (i.e. oligaemic appearance). Cardiac size may be normal or enlarged.</p><h5>Echocardiography/ultrasound</h5><p>Usually the 1<sup>st</sup> line imaging modality in utero. It allows direct visualisation of the anomaly. </p><h5>CT and MRI</h5><p>Allows direct visualisation of anomaly and may typically show a fatty and/or muscular separation of the right atrium from the right ventricle. Cine MRI can offer functional information in addition to anatomy.</p>
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