WHO classification of tumours of soft tissue
Updates to Article Attributes
Body
was changed:
The WHO 2002 classification of soft tissue tumours is as follows:
This however has been revised under the 2013 WHO tissue tumour classification system4.
Adipocytic tumours
Benign
- lipoma 8850/0*
- lipomatosis 8850/0
- lipomatosis of nerve 8850/0
- lipoblastoma/lipoblastomatosis 8881/0
- angiolipoma 8861/0
- myolipoma 8890/0
- chondroid lipoma 8862/0
- extrarenal angiomyolipoma 8860/0
- extra-adrenal myelolipoma 8870/0
- spindle cell lipoma 8857/0
- pleomorphic lipoma 8854/0
- hibernoma 8880/0
Intermediate (locally aggressive)
- atypical lipomatous tumour/well differentiated liposarcoma 8851/3
Malignant
-
liposarcoma:
- dedifferentiated liposarcoma 8858/3
- myxoid liposarcoma 8852/3
- round cell liposarcoma 8853/3
- pleomorphic liposarcoma 8854/3
- mixed-type liposarcoma 8855/3
- liposarcoma, not otherwise specified 8850/3
Fibroblastic/myofibroblastic tumours
Benign
- nodular fasciitis
- proliferative fasciitis
- proliferative myositis
- myositis ossificans
- fibro-osseous pseudotumour of digits
- ischaemic fasciitis
- elastofibroma 8820/0
- fibrous hamartoma of infancy
- myofibroma/myofibromatosis 8824/0
- fibromatosis colli
- juvenile hyaline fibromatosis
- inclusion body fibromatosis
- fibroma of tendon sheath 8810/0
- desmoplastic fibroblastoma 8810/0
- mammary-type myofibroblastoma 8825/0
- calcifying aponeurotic fibroma 8810/0
- angiomyofibroblastoma 8826/0
- cellular angiofibroma 9160/0
- nuchal-type fibroma 8810/0
- Gardner fibroma 8810/0
- calcifying fibrous tumour
- giant cell angiofibroma 9160/0
Intermediate (locally aggressive)
- superficial fibromatoses (palmar/plantar)
- desmoid-type fibromatoses 8821/1
- lipofibromatosis
Intermediate (rarely metastasising)
- solitary fibrous tumour 8815/1
- and haemangiopericytoma 9150/1(incl. lipomatous haemangiopericytoma)
- Inflammatory myofibroblastic tumour 8825/1
- low grade myofibroblastic sarcoma 8825/3
- myxoinflammatory
Malignant
- adult fibrosarcoma 8810/3
- myxofibrosarcoma 8811/3
- low grade fibromyxoid sarcoma 8811/3
- hyalinizing spindle cell tumour
- sclerosing epithelioid fibrosarcoma 8810/3
So called fibrohistiocytic tumours
Benign
- giant cell tumour of tendon sheath 9252/0
- diffuse-type giant cell tumour 9251/0
- deep benign fibrous histiocytoma 8830/0
Intermediate (rarely metastasising)
Malignant
- pleomorphic ‘MFH’/undifferentiated pleomorphic sarcoma 8830/3
- giant cell ‘MFH’/undifferentiated pleomorphic sarcoma with giant cells 8830/3
- inflammatory ‘MFH’/undifferentiated pleomorphic sarcoma withprominent inflammation 8830/3
Smooth muscle tumours
- angioleiomyoma 8894/0
- deep leiomyoma 8890/0
- genital leiomyoma 8890/0
- leiomyosarcoma (excluding skin) 8890/3
Pericytic (perivascular) tumours
- glomus tumour (and variants) 8711/0
- malignant glomus tumour 8711/3
- myopericytoma 8713/1
Skeletal muscle tumours
Benign
-
rhabdomyoma 8900/0
- adult type 8904/0
- fetal type 8903/0
- genital type 8905/0
Malignant
- embryonal rhabdomyosarcoma 8910/3
- (incl. spindle cell, 8912/3
- botryoid (anaplastic) 8910/3
- alveolar rhabdomyosarcoma (incl. solid, anaplastic) 8920/3
- pleomorphic rhabdomyosarcoma 8901/3
Vascular tumours
Benign
- haemangiomas of subcutaenous/deep soft tissue: 9120/0
- capillary haemangioma 9131/0
- cavernous haemangioma 9121/0
- arteriovenous haemangioma 9123/0
- venous haemangioma 9122/0
- intramuscular haemangioma 9132/0
- synovial haemangioma 9120/0
- epithelioid haemangioma 9125/0
- angiomatosis
- lymphangioma 9170/0
Intermediate (locally aggressive)
Intermediate (rarely metastasizing)
- retiform haemangioendothelioma 9135/1
- papillary intralymphatic angioendothelioma 9135/1
- composite haemangioendothelioma 9130/1
- Kaposi sarcoma 9140/3
Malignant
- epithelioid haemangioendothelioma 9133/3
- angiosarcoma of soft tissue 9120/3
Chondro-osseous tumours
- soft tissue chondroma 9220/0
- mesenchymal chondrosarcoma 9240/3
- extraskeletal osteosarcoma 9180/3
Tumours of uncertain differentiation
Benign
- intramuscular myxoma 8840/0 (incl. cellular variant)
- juxta-articular myxoma 8840/0
- deep (‘aggressive’) angiomyxoma 8841/0
- pleomorphic hyalinizing angiectatic tumour
- ectopic hamartomatous thymoma 8587/0
Intermediate (rarely metastasizing)
- angiomatoid fibrous histiocytoma 8836/1
- ossifying fibromyxoid tumour 8842/0 (incl. atypical/malignant)
- mixed tumour 8940/1
- myoepithelioma 8982/1
- parachordoma 9373/1
Malignant
- synovial sarcoma 9040/3
- epithelioid sarcoma 8804/3
- alveolar soft part sarcoma 9581/3
- clear cell sarcoma of soft tissue 9044/3
- extraskeletal myxoid chondrosarcoma 9231/3 ("chordoid" type)
- PNET/extraskeletal Ewing tumour
- pPNET 9364/3
- extraskeletal Ewing tumour 9260/3
- desmoplastic small round cell tumour 8806/3
- extra-renal rhabdoid tumour 8963/3
- malignant mesenchymoma 8990/3
- neoplasms with perivascular epithelioid cell differentiation (PEComa)
- clear cell myomelanocytic tumour
- intimal sarcoma 8800/3
-<p>The <strong>WHO 2002 classification</strong> of <a href="/articles/soft-tissue-tumours">soft tissue tumours</a> is as follows:</p><h5>Adipocytic tumours</h5><h6>Benign</h6><ul>- +<p>The <strong>WHO 2002 classification</strong> of <a href="/articles/soft-tissue-tumours">soft tissue tumours</a> is as follows:</p><p>This however has been revised under the <a title="2013 WHO tissue tumour classification system" href="/articles/2013-who-tissue-tumour-classification-system">2013 WHO tissue tumour classification system</a> <sup>4</sup>.</p><h5>Adipocytic tumours</h5><h6>Benign</h6><ul>
References changed:
- 6. Baheti A, O'Malley R, Kim S et al. Soft-Tissue Sarcomas: An Update for Radiologists Based on the Revised 2013 World Health Organization Classification. AJR Am J Roentgenol. 2016;206(5):924-32. <a href="https://doi.org/10.2214/AJR.15.15498">doi:10.2214/AJR.15.15498</a> - <a href="https://www.ncbi.nlm.nih.gov/pubmed/26998884">Pubmed</a>