Absent infrarenal inferior vena cava
An absent infrarenal inferior vena cava can be congenital, due to the failure of development of the posterior cardinal and supracardinal veins, or acquired, as a result of intrauterine or perinatal inferior vena cava thrombosis.
On this page:
Epidemiology
It is an extremely rare anomaly.
Clinical presentation
The patient may present with symptoms of lower extremity venous insufficiency or idiopathic deep venous thrombosis, particularly in younger patients.
Radiographic features
The non-invasive modalities of choice are contrast enhanced CT or MRI, which are preferred to ultrasound. The gold standard is venography, sometimes performed for surgical planning.
General features include:
- absent infrarenal inferior vena cava with preservation of the suprarenal segment
- common iliac veins may be absent
- external and internal iliac veins drain into the ascending lumbar veins, which drain into the azygos-hemiazygos system
- collateral paraspinal circulation may be present
Related Radiopaedia articles
Anatomy: abdominopelvic
- skeleton of the abdomen and pelvis
- muscles of the abdomen and pelvis
- spaces of the abdomen and pelvis
- anterior abdominal wall
- posterior abdominal wall
-
abdominal cavity
-
peritoneum
- peritoneal ligaments
- mesentery
-
peritoneal spaces
-
supramesocolic space
-
right supramesocolic space
- right subphrenic space
-
right subhepatic space
- anterior right subhepatic space
- posterior right subhepatic space (Morison pouch)
-
lesser sac
- epiploic foramen (of Winslow)
- left supramesocolic space (left perihepatic space)
-
right supramesocolic space
- inframesocolic space
-
supramesocolic space
- inguinal canal (mnemonic)
- Hesselbach triangle
- scrotal sac
- retroperitoneum
-
peritoneum
- pelvic cavity
- perineum
- abdominal and pelvic viscera
- gastrointestinal tract
- spleen
- hepatobiliary system
-
endocrine system
-
adrenal gland
- adrenal vessels
- chromaffin cells
- variants
- pancreas
- organs of Zuckerkandl
-
adrenal gland
-
urinary system
-
kidney
- renal pelvis
- renal sinus
- avascular plane of Brodel
-
variants
- number
- fusion
- location
- shape
- ureter
- urinary bladder
- urethra
- embryology
-
kidney
- male reproductive system
-
female reproductive system
- vulva
- vagina
- uterus
- uterine tubes
- ovaries
- broad ligament (mnemonic)
- variant anatomy
- embryology
- blood supply of the abdomen and pelvis
- arteries
-
abdominal aorta
- inferior phrenic artery
- celiac artery
- superior mesenteric artery
- middle suprarenal artery
- renal artery (variant anatomy)
- gonadal artery (ovarian artery | testicular artery)
- inferior mesenteric artery
- lumbar arteries
- median sacral artery
-
common iliac artery
- external iliac artery
-
internal iliac artery (mnemonic)
- anterior division
- posterior division (mnemonic)
- variant anatomy
-
abdominal aorta
- portal venous system
- veins
- anastomoses
- arterio-arterial anastomoses
- portal-systemic venous collateral pathways
- watershed areas
- arteries
- lymphatics
- innervation of the abdomen and pelvis
- lumbar plexus
-
sacral plexus
- lumbosacral trunk
- sciatic nerve
- superior gluteal nerve
- inferior gluteal nerve
- nerve to piriformis
- perforating cutaneous nerve
- posterior femoral cutaneous nerve
- parasympathetic pelvic splanchnic nerves
- pudendal nerve
- nerve to quadratus femoris and inferior gemellus
- nerve to internal obturator and superior gemellus