An absent infrarenal inferior vena cava (IVC) can be congenital due to failure of development of the posterior cardinal and supracardinal veins, or acquired as result of intrauterine or perinatal inferior vena cava thrombosis.
It is an extremely rare anomaly.
The patient may present with symptoms of lower-extremity venous insufficiency or idiopathic deep venous thrombosis, particularly in younger patients.
The non invasive modality of choice are contrast enhanced CT or MRI, which is preferred over ultrasound. The best invasive imaging modality is venography, particularly done if performed for surgical planning.
General features include:
- 1. Bass JE, Redwine MD, Kramer LA et-al. Spectrum of congenital anomalies of the inferior vena cava: cross-sectional imaging findings. Radiographics. 2000;20 (3): 639-52. doi:10.1148/radiographics.20.3.g00ma09639 - Pubmed citation
- 2. Kandpal H, Sharma R, Gamangatti S et-al. Imaging the inferior vena cava: a road less traveled. Radiographics. 2008;28 (3): 669-89. doi:10.1148/rg.283075101 - Pubmed citation
- 3. Iqbal J, Nagaraju E. Congenital absence of inferior vena cava and thrombosis: a case report. J Med Case Rep. 2008;2 (1): 46. doi:10.1186/1752-1947-2-46 - Free text at pubmed - Pubmed citation